The most common benign cardiac tumor is cardiac myxoma,accounting for around 50% of all primary cardiac tumors. Cardiac myxoma is an uncommon cause ofcardioembolic stroke.Overall,cardioembolic stroke accounts for approximately 30% of all ischemic stroke of which 0.5% of cardioembolic strokes are attributable to a cardiac myxoma.It has an annual incidence of around 0.5 cases per one million people with female predominance. Early diagnosis is necessary to prevent its devastating complications such as embolic stroke and sudden cardiac death.We present a relatively rare case of an acute stroke as a first and only manifestation of an atrial myxoma