The Papillon-Lefèvre syndrome (PLS) is a rare, autosomal recessive disease that manifests with palmoplantar keratoderma and destructive periodontitis resulting in early onset periodontal breakdown in deciduous and permanent dentition. Management of this condition is difficult. Here we report one 11-year-old consanguineous Muslim boy suffering from PLS. After failing to get any benefit from methotrexate, three cycles of acitretin, each for 2 months, were given 1 month apart. In each cycle, acitretin (25 mg) was given every other day. At the end of the third cycle, treatment was stopped for 4 months to observe the extent of relapse. Thereafter, acitretin (25 mg) was given twice weekly for 4 months and then the patient was followed up for 1 year. Treatment with acitretin resulted in excellent improvement of periodontitis, increase in the alveolar bone height, and periodontal attachment. Improvement remained stable at the end of 1-year follow-up. There was excellent (>75%) improvement in keratoderma at the end of active therapy. Mild worsening of palmoplantar keratoderma was noticed whenever the drug was stopped. It improved when the drug was restarted. Other areas remained stable. At the end of 1-year follow-up, good improvement (50%) in palmoplantar keratoderma was achieved.

The study showed there was no significant difference (P > 0.05) between the average decayed extracted filled teeth (deft)/DMFT for boys and girls in deciduous and permanent dentition. But in mixed dentition this value for the boys was significantly higher (P < 0.001) than girls. 'Z' values were found to be non significant when compared mild, moderate and severe gingivitis between boys and girls in each dentition group, but mild gingivitis significantly increases from deciduous dentition to mixed to permanent dentition (P <0.001).

Context:Facial analysis is the first step in the evaluation of patients with orthodontic, cosmetic, or reconstructive procedures of the face, and one of the most important components of orthodontic diagnosis and treatment planning. It is a well-established fact that human faces differ from one another on the basis of race and ethnicity. The study will provide the aesthetic guidelines to assess the facial discrepancy in Bengali children to develop a proper treatment plan.Aims:To find out the mean values for selective linear measurements on the facial soft tissue of Bengali children, to demonstrate gender differences in the measurements.Materials and Methods:A cross-sectional study was done on 250 Bengali children of 6-14 years age, by measuring certain identified facial landmarks using a digital caliper.Statistical Analysis Used:Analytical statistical method with the help of student's t-test was used to determine mean values, standard deviation, and gender differences in the measurements using SPSS version 11.0.Results:In 6-8 years age group, male's average inter-endocanthion distance was significantly higher than that of females (P < 0.05), whereas in 12-14 years age group, the same parameter for females was significantly higher than that of males (P < 0.001). In 9-11 years age group, the average distance of exocanthion to exocanthion was higher for males compared to females, but the difference was not significant at 5% level (P > 0.05), though for 87% of cases, it was significant (P = 0.13). Total facial height for male subject was significantly high compared to that of females (P < 0.001) in 12-14 years age group.Conclusions:The study will provide the aesthetic guidelines to assess the facial discrepancy in Bengali children and provide a proper treatment plan through a simple and economically reasonable soft tissue analysis method.

There was a significant difference between caries and control group in different patterns and number of "tri radii on fingers" in fingers, the percentage of patterns on all palmar areas, total number of triradii on palm and main line index. Perhaps more systematic larger samples consisting of different genetic population are necessary to verify the conclusion.

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