We describe two cases of Rosai-Dorfman disease. One of them had commonly described cervical adenopathy and the second with the very rare bilateral orbital involvement. Both our cases required treatment with steroids because of the danger of pressure symptoms and disfigurement and multiple episodes of high fever in one of them.

Ghosal type hemato-diaphyseal dysplasia is a recently described clinical entity. The authors describe such a case with severe anemia requiring transfusions and with clinical and radiological evidence of diaphyseal dysplasia. Very few such cases are reported in world literature.

A child with Jervell-Lange Nielsen syndrome is presented from Kolkata. Family study showed that the other family members are suffering from long QT syndrome. The child had frequent syncopal attack and very prolonged QT interval requiring left cardiac sympathetic denervation and beta-blocker therapy as patient could not afford implantable defibrillator and cardiac pacing.

Gastric outlet obstruction due to tuberculosis causing persistent vomiting is rare in occurrence. Abdominal tuberculosis is most common at ileocecal junction. This case presents with gastric outlet obstruction due to extra luminal compression by an enlarged lymph node around first part of duodenum with duodenal involvement. As the organism is acid fast and number of lymph node in this area is scanty, occurrence of tuberculosis in this region is very uncommon. As per literature, data related to such type of presentation of abdominal tuberculosis is very rare.

No abstract