Schwannomas are rare tumors originating from Schwann cells, producing a nonspecific clinical picture that depends on the location of the tumor. The retroperitoneal location is infrequent, its incidence varies from 1% to 5% of all neoplasms in this site. The definitive diagnosis is histopathological, but it is supported by imaging studies. The definitive treatment is complete extirpation. We present the case of a 24-year-old man with no relevant pathological history who presented with abdominal pain and paresthesia in the lower limb, treated in the department of oncological surgery. The imaging studies showed a retroperitoneal tumor whose histopathological diagnosis was schwannoma with positive immunohistochemistry for S-100. Exploratory laparotomy and complete tumor resection were performed, with complete posterior recovery. After three years of follow-up, he was asymptomatic.