Neurofibromatosis type 1 (NF1) or Von Recklinghausen's disease is a rare genetic disorder characterized by the development of multiple noncancerous (benign) tumors of nerves and skin (neurofibromas) and areas of abnormally decreased or increased coloration of the skin. We present a case of 11-year-old boy with NF-1. The disease started in childhood with the appearance of multiple hyper pigmented skin macules. The boy presents excruciating lower back pain and lumbar scoliosis. The diagnosis NF-1 was made according to the presence of two or more diagnostic criteria of the National Institute of Health Consensus Development Conference. NF1 is a multisystem disorder requiring management by multiple disciplines, often coordinated through a primary care physician or a geneticist and dermatologist.

ObjectiveTo determine the efficiency of the interscrotal approach to inguinoscrotal pathologies.Patients and methodsWe report the use of the interscrotal approach in 21 boys, from September 2012 to November 2013, operated using an interscrotal access through a vertical incision on the median raphe.ResultsThe approach was used for bilateral inguinal hernia (48%), bilateral ectopic testis (19%), torsion of the spermatic cord (19%), testicular biopsy (10%) and webbing of the penis (5%).ConclusionInter-scrotal access is an option for inguinoscrotal pathologies, with the advantages of a single incision, much less dissection and disruption of tissue, and greater comfort for the ‘day-case’ child.

Vulvar fibroma is a rare and the most common benign tumor that is predominantly found in women of reproductive age group. When located in the vulva, they occur more often in the labia majora and less frequently in the labia minora, clitoris, vestibule, and posterior commissure. In tumors of long clinical duration, ulcerations with superficial bleeding, often due to repeated trauma, are often observed. This case report describes a unique case of giant soft fibroma located in labia majora in a girl aged 03 years.

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