A. Involvement of sural nerve in neuronal ceroid-lipofuscinoses. Neuropadiatrie Band 3:98-110(1973). Findings in sural nerve biopsies in two patients with neuronal ceroid lipofuscinosis are described. In Schwann-cells and in smooth muscle cells of vessels curvilinear-and fingerprintmaterial were demonstrated. The report discusses the significance of these findings. The clinical findings were in agreement with a diagnosis of late infantile and juvenile type respectively. Ultrastructurally there were signs of transitions between the two types of inclusion. The place of sural nerve biopsy in the range of diagnostic procedures in progressive neurological diseases in discussed.Batten's disease ceroid-lipofuscinoses curvilinear bodies fingerprintmaterial sural nerve biopsy

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Two patients with the clinical picture of a late infantile and juvenile amaurotic familial idiocy (Batten's disease) have been examined electron microscopically. The typical cytoplasmic inclusion bodies in the Schwann cells of the sural nerve supported this clinical diagnosis. The importance of sural nerve biopsy in patients with a cerebroretinal degeneration is discussed.

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