Background: Intravascular papillary endothelial hyperplasia (IPEH) or Masson´s tumor is a benign vascular lesion consisting of a reactive proliferation of the endothelial cells with papillary formations that arise in organizing thrombus. It is most commonly a cutaneous or subcutaneous lesion. Although it has also occurred in many locations, the sinonasal presentation is extremely rare. Its clinical presentation is unspecific and the diagnosis is through histolopathological analysis. The main significance of IPEH is its clinical and microscopic resemblance to angiosarcoma and the possibility of a misdiagnosis.