Neuroblastoma is the most frequent solid extracranial neoplasia in children and is responsible for about 15% of all pediatric cancer deaths. It is an embryonal malignancy of the postganglionic sympathetic nervous system, which generally arises in the adrenal gland. 96% of cases occurs below 10 years age group and is slightly more common in Caucasian boys. The primary renal neuroblastoma is rare, corresponding to 30-35% of all neuroblastomas. The diagnosis of neuroblastoma by imaging (ultrasound, CT scan, and MRI) features high accuracy and turns the medicine´s comprehension completely possible, and effective. Neuroblastoma signs and symptoms vary widely, depending on the size of the tumor, where it is, how far it has spread, and if the tumor cells secrete hormones. Here we report a case of a two-years-old male patient, who was hospitalized at first with a right hip pain and proceed the treatment of arthritis. After that, some suggestive symptoms started to be presented in addition to the radiology methods, turning the diagnosis possible and making the correct procedures.