Three children with different types of dysplasia epiphysealis hemimelica in the ankle are described. It is an uncommon disorder belonging to the group of osteochondromatoses. The disease occurs in young children and is localized mainly in the ankle and knee joints. The clinical symptoms, localization, and roentgenograms are most important for reaching a diagnosis. A pathological-anatomical examination is a necessity in order to exclude malignancy. Early surgical treatment is recommended, but complete cure is seldom achieved.