Myxomas are generally polypoid, often pedun-culated, rarely sessile, and round or oval, with smoothor soft lobulated surface. The tumor size ranges from1 to 15 cm in diameter; mostly are 5 to 6 cm. Mostmyxomas originate from left atrium. Right-sidedmyxomas are extremely rare and can present withnonspecific signs and symptoms. Despite the lackof symptoms and signs they should have a surgicalresection. Surgical removal of the tumors should beperformed as soon as possible because the long termprognosis is excellent and recurrences are rare.This paper reports a case of right atrial myxoma inan 11-year-old girl.