Highlights Mucocele of the appendix is a rare lesion of the appendix with a incidence of 0.3 to 0.7% of the appendectomies. Clinical presentation is usually vague and asymptomatic in quarter of patients. It requires keen mindset for proper evaluation. Prudent planning is must to avoid inadequate treatment which adds in the morbidity of patient significantly. And there is always risk of development of pseudomyxoma peritonei.