In this single-center medical record review, almost half of the patients referred for diagnosis of IgG4-RD were found to have a mimic of the disease.• Based on specific cases and findings in our cohort, it is important to note that elevated serum IgG4 levels in isolation are not diagnostic for the disease. • A repeat tissue biopsy should be done in the majority of cases with atypical clinical presentation and those that do not respond to glucocorticoids.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.