Otosclerosis is an important condition for the otorhinolaryngologist, and often in (differential) diagnosis and therapy challenging disease. Although a causal therapy option does not exist until today, if the diagnosis is correct, an operative or apparative hearing rehabilitation with very high chances of success can be promised. In addition to hearing aids surgical treatment with passive implants as a standard therapy, and in special cases also the implantation of active middle ear implants or cochlear implants, in advanced otosclerosis with significant involvement of the inner ear, are of importance. Knowledge of the definition, pathogenesis, diagnostics and in particular of the differential diagnosis as well as the current conservative and operative therapeutic limits are indispensable for the indication and selection of the optimal treatment path.In a two-part presentation, the current specialist medical knowledge of the disease in diagnosis and therapy is summarized. In addition to modern diagnostic procedures, aspects of therapy and prognosis are considered in a second article. This article therefore primarily refers to continuing education for residents in training and for young specialists.

ZusammenfassungFür die – oft in Diagnostik und Therapie anspruchsvolle – Otosklerose kann bei richtiger Diagnosestellung eine operative oder apparative Hörrehabilitation mit sehr hohen Erfolgschancen in Aussicht gestellt werden. Der erste Teil des Fortbildungsbeitrags umfasste Grundlagen, Diagnostik und Differenzialdiagnostik, im zweiten Teil soll auf therapeutische Aspekte und Nachsorge eingegangen werden.

The rate of recruitment was lower than expected. Depending on the case number calculations for the patient groups identified in the study for whom BET might be particularly beneficial, multicenter studies in specific disease groups may follow.

The limited experience of this study suggests that the NiTiFLEX® stapes prosthesis is a successful further development of the Soft CliP® technique with very good intraoperative handling qualities. While long-term results from larger studies are needed, this case series demonstrates that the hearing outcome is comparable to other prostheses.