No abstract

Feta l rhabdotnyoma is not generally considered part of nevoid basal cell carcinoma syn drome. How ever. a review ofthe literature revealedfive patients with this sy ndrome 11' 170 also had feta l rhabdomy omas in various locations. We report thefirstpatient with nevoid basal cell carcinotna syndrotne and afetal rhabdoiny oma ofthe tongu e. We reconunend that embryonal rhabdontyosarcoma be ni/ed out to avoid ove rly aggressive treatment ofthese patients .