The main cause of acquired heart disease in children in developing countries is Kawasaki syndrome. Approximately 25% of patients develop coronary aneurysms for not receiving treatment, however, those who receive it early, cause that proportion tends to decrease by 5%. By means of the proposal of a documentary design, with the present revision the main objective is defined to carry out an updated summary referring to the treatment of Kawasaki syndrome, considering for this the need to conceptualize it and at the same time describe the most outstanding aspects such as the etiological ones, pathological and genetic, as well as its diagnosis, in order to make available a current bibliographic content on this pathology, useful both for the attending physician and for any other interested in knowing about said disease and its treatment. It is concluded by highlighting the importance of an accurate and timely diagnosis, which is ultimately the transcendental when establishing the right treatment in the acute phase, in order to minimize the incidence of coronary alterations and, in turn, the long-term consequences term presented.