Aicardi syndrome is a rare congenital anomaly characterized by infantile spasms, agenesis of the corpus callosum, and chorioretinal lacunae. This syndrome has been observed only in females. A case of Aicardi syndrome with cleft palate is reported. A six-month-old girl was given a diagnosis of Aicardi syndrome with cleft palate. At 3 years 4 months of age, when the patient weighed 11.3kg, we performed a push-back operation without complications. She is now 8 years old and is not able to use intelligent words. Nearly 200 patients with Aicardi syndrome have been described in the literature. This report is the seventh case associated with cleft lip and palate, and the second case to undergo palatoplasty.
We describe a patient with a blood boil of the maxillary sinus that protruded through the alveolar ridge into the oral cavity. The patient was a 55-year-old man who visited our department because of a mass lesion in the left side of the maxilla. On X-ray film, the lesion occupied the left maxillary sinus, MRI findings suggested hemangioma. The lesion was diagnosed as heamangioma on biopsy. To prevent massive bleeding during surgery, selective embolization of the left maxillary artery and facial artery was performed 2 days before the operation. Consequently, the lesion could be resected safely. There have been no signs of recurrence. Since tha surgical specimen consisted of fibrin and blood components and showed no pathologic feature of hemangioma, the patient was given a definitive diagnosis of a blood boil of the maxillary sinus.
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