We report on the rare case of partial anomalous return of four pulmonary veins in the right atrium and superior vena cava with intact interatrial septum in a five-year-old child. There were few symptoms in contrast with the left ventricular output dependent on the flow of the left upper lobe vein and from the lingula. Reduced compliance to the left led to a severe picture of pulmonary venocapillary hypertension in the immediate postoperative period, mitigated by an 8-mm interatrial septal defect. The patient progressed well after the intervention. systolic impulses, constant split second sound and a mild systolic murmur in the pulmanary area. The liver was normal. Partial AnomalousThe electrocardiogram showed sinus rhythm, right ventricular diastolic overload, multiphase QRS complex in V1, thickened S-waves in I, L and V4 to V6, and duration of 0.11". Chest radiography showed mild cardiomegaly at the expense of the right cavities, convex medial arch and prominent pulmonary vasculature. Echocardiogram showed a discreet enlargement of right cavities, right PAPVR in the right atrium and in the right superior vena cava (RSVC). The left superior vena cava and the left inferior pulmonary vein drained to the coronary sinus. Interatrial septum was intact. Surgical treatment was performed with extracorporeal circulation (ECC) under hypothermia at 24 o C. Myocardial protection was performed with hypothermal blood cardioplegic solution (4 o C) every 30 minutes. Through a longitudinal right atriotomy extended to RSVC, the intact atrial septum was resected, and the reduced left atrium was visualized. We observed that the vein of the right upper lobe drained into the RSVC and those of the right medial and inferior lobe drained into the right atrium. The LLL vein connected through the same drainage orifice of the right lower lobe vein, and the LUL and lingula veins together drained in the usual way into the left atrium. The anomalous vein were cannulated with autologous pericardium tissue to the left atrium and to the RSVC enlarged with bovine pericardium graft. Anoxic cardiac arrest last 105 minutes, and extracorporeal circulatory support last 170 minutes. We observed suprasystemic pressure in the right ventricle and hypertension (50 mm Hg) in the left atrium. Transesophageal echocardiogram (TEC) revealed moderate mitral insufficiency and left ventricular dysfunction. The extracorporeal circulation was reestablished for an additional 35 minutes, for an 8-mm atrioseptectomy, performed on the autologous pericardium graft. There was then an improvement in ventricular function and in mitral regurgitation, which was confirmed on TEC.