Desmoid-type fibromatosis (DTF) is a rare locally aggressive soft tissue neoplasm without metastatic potential. Here, we report a very rare sporadic case of an intracranial supratentorial extradural DTF measuring 82 mm in a 1-year-old girl, that recurred twice following surgery over the course of 16 months, requiring two other surgeries. In three surgeries, we resected a huge tumor with the dura which was thought to be tumor origin and removed this tumor infiltrated the frontal skull base by drilling widely. Furthermore, we treated the tumor invading the bone flap using liquid nitrogen for 20 minutes, and subsequently used it to perform a cranioplasty. This tumor has not recurred for past 8 months. DTF invading the skull base is prone to recurrence, and liquid nitrogen treatment is considered to be effective in pediatric patients, who need cranioplasty with tumor-infiltrating autologous bone flaps.

Preoperative transarterial feeder embolization (TAE) may contribute to the safe surgical removal of hyper vascular tumors such as cerebellar hemangioblastomas (CHBs). We examined the usefulness of preoperative TAE of CHBs in our series. Methods:We retrospectively analyzed the results of treatment in seven patients with CHBs who had undergone preoperative TAE and subsequent surgery in our hospital between 2005 and 2015 (four males and three females, mean age: 45 years). Results:The embolized feeders consisted of the posterior inferior cerebellar artery in five patients, superior cerebellar artery (SCA) in one patient, and occipital artery (OA) in one patient. The embolic materials consisted of polyvinyl alcohol (PVA) in two patients, nbutyl2cyanoacrylate (NBCA) in four patients, and the combination of PVA and NBCA in one patient. Surgery was performed 1-4 days after embolization. The mean volume of intraoperative blood loss was 593 mL.In all patients, total surgical removal of the tumor was possible in the absence of nonautologous blood transfusion.Furthermore, embolic blood vessels could be identified during surgery in all patients, contributing to intraoperative orientation. Periprocedural complication related to TAE, cerebellar infarction related to embolicmaterial migration into a normal blood vessel occurred in one patient (13%). Conclusion:The results suggest that preoperative TAE of CHBs using NBCA contributes to a decrease in the volume of intraoperative blood loss, intraoperative orientation, and safe surgical removal of CHBs.