Neutrophilic eccrine hidradenitis (NEH) is a distinctive dermatosis occurring in patients with malignancy or undergoing chemotherapy. This disorder is characterized by a neutrophilic infiltrate around the eccrine glands and secretory coils, and is associated with necrosis. It must be distinguished from infections, drug eruptions, malignancies or other forms of skin diseases. As it is a self-limiting condition, establishing the diagnosis will avoid unnecessary investigations and treatment. Here we report a case of NEH in a 40-year-old woman suspected to be due to carbamazepine.

Porokeratosis is a disorder of epidermal proliferation in which many different clinical variants can be distinguished. Herein we report a rare case of porokeratosis involving almost all parts of the body with simultaneous occurrence of various forms of the disease in the same individual (classical porokeratosis of Mibelli, disseminated superficial actinic porokeratosis, hypertrophic porokeratosis, and genital porokeratosis).

A constriction band around little finger. Well-defined transgradient margins [ Figure 1a-c].Warty and linear plaques over the dorsal aspects of the hands feet.Ichthyosis of the lower limb and multiple discharging sinuses at the hip were seen in this patient. Hair and nails were normal.The histopathological findings consisted of marked hyperkeratosis, acanthosis, and focal hypergranulosis.Though the patient did not have any complaints of sensory deficit, we asked for an audiogram which revealed mild-to-moderate sensory neural deficits in both ears.Her chest radiograph showed right mid and lower zone consolidation. • Radiograph of the pelvis showed left sacroiliac joint-osteomyelitis.Our patient was put on category I antitubercular therapy and topical keratolytic agents DISCUSSIONIn 1929, Vohwinkel first described this syndrome in a 24-year-old woman who had a diffuse honeycombed palmar and plantar keratosis, in addition to distal interphalangeal constrictions since 2 years of age. ABSTRACTVohwinkel's syndrome is an autosomal dominant type of palmoplantar keratoderma characterized by honeycomb appearance, pseudoainhum leading to autoamputation, stellate keratosis on knuckles, and associated with sensorineural deafness.An Ichthyotic variant is recently described .We report a rare case of Vohwinkels syndrome with ichthyosis.

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