Since management of parturients with uncorrected tetralogy of Fallot reported until now lacks advanced cardiac haemodynamic monitoring, we aimed to present anaesthetic management of a parturient with uncorrected tetralogy of Fallot scheduled for caesarean section by addressing the challenges in the management based on the advanced haemodynamic monitoring due to the expected high-risk maternal morbidity and mortality in this particular case. Hereby, we provided haemodynamic stability with little requirement for vasopressor medication by using low-dose combined spinal epidural anaesthesia in a parturient with uncorrected tetralogy of Fallot scheduled to undergo caesarean delivery.