IntroductionIn this report we discuss an unusual cause of subarachnoid haemorrhage in association with neurofibromatosis.Case presentationA previously fit 55-year-old man developed sudden onset headache with loss of consciousness. He was comatose on admission with no focal neurological signs. Numerous neurofibromas and café-au-lait patches were noted, indicating neurofibromatosis type 1 which had not been previously diagnosed. Computer Tomography brain revealed a grade IV subarachnoid haemorrhage in association with numerous vascular lesions on cerebral angiography.ConclusionA rare cause of subarachnoid haemorrhages was identified and is discussed in detail.