Otologic manifestations are known to occur in patients with idiopathic intracranial hypertension (IIH), but the occurrence of sensorineural hearing loss, especially in pediatric populations, has been addressed in only a few reports. Here, we describe a pediatric patient who presented with IIH and severe bilateral hearing loss. The patient's hearing loss was diagnosed as a form of auditory neuropathy (AN) and resolved after prompt treatment of the increased intracranial pressure. This case points to a possible association between IIH and AN and suggests that IIH may potentially be a reversible cause of AN spectrum disorder.
Objectives: To evaluate outcomes of BAHA Connect 1 and BAHA Attract 1 implantations, and to examine the prognostic utility of a preimplantation Softband 1 -attached processor trial. Study Design: Retrospective case review Setting: Tertiary referral center. Patients: Patients who underwent Connect 1 (19 ears) and Attract 1 (25 ears) implantation between 2007 and 2017. Intervention: BAHA 1 implantation. Main Outcome Measures: Unaided air conduction (AC), bone conduction (BC), and speech reception thresholds (SRTs), as well as free field (FF) aided with Softband 1attached processor and with implant-attached processor thresholds. Results: Serviceable implant-attached processor PTA 0.5,1,2 kHz ( 35 dB HL) was achieved in 89 and 88% of the Connect 1 and the Attract 1 ears, respectively, while at 4 kHz this was achieved in 68 and 32% of the Connect 1 and the Attract 1 ears, respectively ( p ¼ 0.032). Significantly more Connect 1 ears showed alignment between FF aided with implant-attached processors thresholds and BC thresholds. The alignment between the Softband 1 -attached processors thresholds and implant-attached processors thresholds was similar in the two groups. Both groups exhibited similar positive improvement in the quality of life questionnaires Conclusions: Accessibility to sound with the implantattached processor is well predicted by the pre-implantation Softband 1 trial, both in the BAHA Connect 1 and in the BAHA Attract 1 ears. Hearing rehabilitation targets at 0.5, 1, and 2 kHz are met by most Connect 1 and Attract 1 ears, while at 4 kHz the outcome with Attract 1 is poorer. This information should be presented to the patient during consultation prior to a decision as to the type of BAHA 1 device to be implanted.
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