Vestibular Shwannomas are responsible for 80-90% of the cerebelar-pontine angle tumors and their incidence is of 0.8 to 20.5% of all tumors. Unilateral and progressive hearing loss is the most frequent and premature symptom, and tinnitus is the second most common complaint. Only 5% of the patients have normal audiograms. In this case the patient complained of ipsilateral facial numbness and weak blink, posterior pinna hypoesthesia (Hitzelberger +), tear reduction and positive Romberg test. He also had mouth twisting but no other involvement of other cranial nerves. Hearing acuity was normal.

A Síndrome de Kartagener é causada por uma doença autossômica recessiva rara, que apresenta uma tríade composta por pansinusite crônica, bronquiectasia e situs inversus com dextrocardia. A incidência desta desordem genética é estimada em 1/25.000. Nosso objetivo é, neste trabalho, aduzir dados novos àqueles que pesquisam o assunto, para que estejam atentos, acompanhando os pacientes e esperando o aparecimento eventual desta malformação. Foram realizadas tomografias computadorizadas do tórax, abdome e crânio, além da tomografia computadorizada de alta resolução do tórax, audiometria, imitanciometria e vídeo-naso-fibroscopia.

Vest ibular Shwannomas are responsible for 80-90% of the cerebelar-pontine angle tumors and their incidence is of 0.8 to 20.5% of all tumors. Unilateral and progressive hearing loss is the most frequent and premature symptom, and tinnitus is the second most common complaint. Only 5% of the patients have normal audiograms. In this case the patient complained of ipsilateral facial numbness and weak blink, posterior pinna hypoesthesia (Hitzelberger +), tear reduction and positive Romberg test. He also had mouth twisting but no other involvement of other cranial nerves. Hearing acuity was normal.