Stillbirth continues to be one of the most devastating events for patients and doctors. Efforts for determining the cause of death should always be made, to prevent endangering future pregnancies and obstetric complications. A comprehensive approach that includes autopsy, placental examination and ancillary studies such as microbiology and toxicology are the best way of establishing the cause of stillbirth. Careful examination of the placenta and umbilical cord is imperative since they are associated with common causes of stillbirth. Here we present a case of umbilical vein varix that presented with associated complications that resulted in intrauterine fetal death.