Ectopic kidney (renal ectopia) is a kidney that is not located in its usual position. It has an incidence of approximately 0.11% in general population and incidence of pelvic kidney is 0.0005% and ectopic kidney with a renal stone is rarer finding with very few reported cases. Mostly patient are asymptomatic and diagnosed incidentally, many a time it only presents as a lump during abdominal examination, patient may come with urinary complaints such as urine blockage, infection or urinary stone. Here we report a case of ectopic kidney with renal calculi and X Ray KUB showed the presence of stone in the pelvis which was later confirmed for it to be in the kidney by ultrasonography, CTand IVP which was managed by open pyelolithotomy with DJ stent placement using midline incision.