The symptoms and signs of congenital heart disease and patients who have prostheses and / or pacemakers placed must be assessed by the stomatologic dentistry specialist, for this they must be trained and prepared in their actions to avoid the risk of complications and in relation to the multidisciplinary team, since These patients are becoming more frequent. The stomatologic dentistry specialist in must apply a correct and attentive semiological examination, since in the same patient one or more syndromes and one or more pathologies can be presented KEY WORDS: dentistry, congenital heart disease, patient management ResumenLos síntomas y signos de las cardiopatías congénitas y pacientes que tienen colocadas prótesis y/o marcapasos deben ser valorados por el Odontoestomatólogo, para ello deben estar capacitados y preparados en su accionar para evitar el riesgo de complicaciones y en relación con el equipo multidisciplinario, ya que estos pacientes son cada vez más frecuentes. El Odontoestomatólogo debe aplicar un correcto y atento examen semiológico, ya que en un mismo paciente se pueden presentar uno o más síndromes y una o más patologías. PALABRAS CLAVE: odontología, cardiopatías congénitas, manejo pacienteMercado Rev

Ectodermal dysplasia is a rare inherited disorder distinguished by the not normal development of certain structures of ectodermal origin. The hypohydrotic ectodermal dysplasia has an autosomal recessive or X-linked inheritance, the latter being the most frequent. Patients with ectodermal dysplasia are patients who require a multidisciplinary approach to their treatment. It is of great importance that the patient is treated at an early age so that their self-esteem and their integration into society are not affected. Due to the oral characteristics of the DEH, the most common treatment is the elaboration of total prostheses, although the clinician may face various difficulties such as the poor development of alveolar processes and dry mouth, resulting from the poor or no salivary secretion.

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