Sturge (1879)' fast described the clinical features of the disease, whereas Weber (1929) 2 demonstrated the pattern of intra-cranial caleitication and named it encephalofacial angiomatosis. The characteristic features include an angiomatous malformation of the skin, usually in the distribution of the branches of trigeminal nerve and a similar vascular anomaly of the ipsilateral cerebral hemisphere. The resultant ischaemia gives rise to convulsions, hemiplegia, hemicerebral-atrophy and mental retardation.

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