The authors describe a five year-old plump looking female child with poorly controlled type 1 diabetes mellitus, hepatomegaly and growth retardation. Contrary to the usual phenotype of thin emaciated appearance in type 1 diabetes mellitus, the presence of above features should make one suspect Mauriac syndrome. Since the basis of this syndrome is poor metabolic control, early recognition is important. The authors emphasize the importance of optimal glycaemic control in preventing complications associated with Mauriac syndrome.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.