Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented.

Langerhans cell sarcoma (LCS) is a highly malignant neoplasm exhibiting<b> </b>aggressive clinical behavior. In this study, we aimed to explore the current status and trends of research on LCS by doing a bibliometric analysis. Data on LCS were retrieved from the Web of Science database and a bibliometric analysis was conducted to measure the impact of publications, authors, organizations, and countries. Different software packages, including BiblioAnalytics, Bibliomaster, MS Excel, MS Access, VOSviewer, Biblioshiny, Power BI, and an online visualization platform were used for analysis and visualization in the present study. A total of 96 publications were included in the present bibliometric analysis. Authors “Lebbe C”, “Lorillon G”, “Mourah S”, and “Tazi A” received the highest number of citations, and the journal “Histopathology” received the highest number of citations. The outstanding organization was the Mayo Clinic in the USA with the highest number of 5 publications and the highest number of 175 citations. Japan and the USA were the outstanding countries that contributed to the research on LCS. Current literature on LCS is minimal, which stresses the need for more research productivity, especially within areas regarding diagnosis and immunohistochemical staining with CD markers for this pathology.

Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors of peculiar cells that are focally associated with blood vessels, and generally have a distinctive bi-phenotypic expression of both smooth muscle and melanocytic markers. There are several entities in the PEComa family, including tumors that arise in the soft tissues and viscera. Frequently affected organs include the lungs (sugar tumors), uterus, broad ligament, colon, small bowel, liver, and pancreas. Ulcerative colitis (UC) has been associated with the development of tumors, especially colorectal and hepatobiliary carcinomas. Rare cases of UC have been reported in the PEComa family of tumors, but none in the pancreas. Here, we present a case study of a 27-year-old female patient with a history of UC who developed PEComa of the pancreas, a unique association that has not been previously reported. We also review reported cases of PEComas in the pancreas, as well as PEComas at all anatomic sites associated with UC.