No abstract

No abstract

Parry-Romberg syndrome or progressive facial hemiatrophy is a rare clinical entity of an unknown etiology. We present the case of a 57-year-old Chinese woman with Parry-Romberg syndrome and hemifacial spasm both on the right side. Its association was not reported before. In our report of Parry-Romberg syndrome with hemifacial spasm, we try to explore whether there were some relations between the 2 diseases. We found an offending vessel compressing the root exit zone of the facial nerve and no evidence of vessel compression at ipsilateral trigeminal nerve motor rootlet.

Objectives To develop a novel grading system and appropriate surgical approaches for patients with diffuse type tensosynovial giant cell tumor (D‐TGCT) of the temporal bone. Study Design Retrospective cohort study. Methods We retrospectively reviewed 31 patients with temporal bone D‐TGCT between June 2012 and July 2021. All patients underwent comprehensive clinical evaluations, including clinical presentations, hearing threshold, imaging studies, surgical approaches, and prognosis. A grading system was developed based on the tumor location and adjacent neurovascular structures involvement according to imaging and intraoperative findings. Results In this study, grade II tumors were the most common (13/31), followed by grades I (7/31), III (7/31), and IV (4/31) tumors. Seven grade I patients received the subtemporal middle cranial fossa approach (SMCF) combined with the canal wall up mastoidectomy and tympanoplasty (CWUT). Nine grade II patients underwent SMCF combined with subtotal petrosectomy (SPTR), and four grade II patients underwent SMCF combined with CWUT. Seven grade III patients received SMCF combined with SPTR and dura mater reconstruction, and four grade IV patients underwent infratemporal fossa approach type B. Gross total resection was achieved in all patients, and the median follow‐up time was 30.1 months (range, 4–96 months). Three patients (one grade II, one grade III, and one grade IV) had recurrence during follow‐up, and the patient with grade III tumor had two recurrences. Conclusions Gross total resection is the first‐line treatment for patients with D‐TGCT of the temporal bone. This novel grading system enables surgeons to select optimal surgical strategy. Long‐term follow‐up is mandatory postoperatively. Level of Evidence 4 Laryngoscope, 132:1275–1284, 2022