A double aortic arch presenting in the 7th decade of life

Vatish, Jamie; McCarthy, Robert C.; Perriss, Richard

doi:10.1093/jscr/rjt081

Cited by 5 publications

(5 citation statements)

References 8 publications

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“…Presentation of DAA in an adult can occur from symptoms similar to those in childhood, especially from dysphagia due to compression of the esophagus. Reports of asymptomatic adults with DAA (such as our case) are sparse in the literature [4][5][6]. Certain factors increase the likelihood of diagnosing DAA in adulthood rather than childhood.…”

Section: Discussionmentioning

confidence: 99%

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Double Aortic Arch in an Asymptomatic Adult

Lee¹,

Shah²,

Ku³

et al. 2023

Cureus

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We present a rare double aortic arch (DAA) diagnosis incidentally on CT in a 60-year-old male who presented with pneumonia. DAA is a vascular ring that typically manifests in infants or children due to compression of the esophagus or trachea, resulting in dysphagia or dyspnea. Diagnosis of DAA in adulthood is usually due to the delayed emergence of obstructive symptoms. We present a case of DAA in an adult patient without dysphagia or dyspnea. We discuss factors that can lead to the presentation of DAA in adults. These include an absence of associated congenital disabilities, insufficient tracheal or esophageal constriction in childhood and the onset of compressive symptoms later in life from decreased vascular compliance.

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Section: Discussionmentioning

confidence: 99%

“…DAA is exceedingly rare, with one in 15,000 births accounting for only 1% of all congenital heart diseases [ 4 ]. The majority of DAA cases are diagnosed in infancy or childhood.…”

Section: Discussionmentioning

confidence: 99%

Double Aortic Arch in an Asymptomatic Adult

Lee¹,

Shah²,

Ku³

et al. 2023

Cureus

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“…It has been reported that its pathogenesis is related to genetic factors and its correlation with chromosomal abnormalities is as high as 24% [7]. McElhinney et al studied 66 cases of 22q11 chromosome microdeletions, 14% of which had clinical symptoms of DAA, which became an important etiological factor in the congenital double aortic arch [8, 9]. DAA often combines with other cardiovascular malformations, TOF is the most common [10].…”

Section: Discussionmentioning

confidence: 99%

Diagnosis and surgical repair of congenital double aortic arch in infants

Yang

Jin

Pan

et al. 2019

J Cardiothorac Surg

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Objectives Double aortic arch (DAA) is a rare congenital vascular malformation. This study aims to summarize the experience of diagnosis and surgical treatment for congenital double aortic arch. Methods The clinical data of 24 cases with double aortic arch (DAA) from January 2008 to January 2018 in our hospital was reviewed retrospectively. Results A total of 24 cases, including 12 patients with isolated DAA and 12 patients with DAA and associated intracardiac defects were identified. There were 14 males and 10 females, with an average age of 11 months. The associated intracardiac malformations included ventricular septal defect (VSD), atrial septal defect (ASD), patent ductus arteriosus (PDA), tetralogy of Fallot (TOF), transposition of the great arteries (TGA), pulmonary stenosis (PS), and patent foramen ovale (PFO). Of the 12 patients with DAA and intracardiac malformations, 7 patients underwent intracardiac repair simultaneously, however, 3 patients underwent isolated double aortic arch correction. One patient with DAA and TGA underwent surgical correction of congenital vascular ring at the first stage, and the arterial switch operation was performed at the second stage. The clinical outcomes of 23 patients were promising, however, in one patient, parents decided not to do the surgery due to personal reasons. The average follow-up time was 35 months. Conclusions Tracheal and esophageal compression are commonly seen in patients with DAA, however could be relieved significantly after surgery. In particular cases, the simultaneous intracardiac defects repair could be performed. Misdiagnosis was easily established with isolated echocardiography. Fortunately, the correct diagnosis of DAA and associated intracardiac defects could be established with the use of combined chest computed tomography.

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“…(11,12) The literature reported very few cases diagnosed late or during adolescence or adulthood. (10,(13)(14)(15)(16)(17)(18) Clinically most of the anatomical variants are usually symptomatic especially that are associated with congenital heart defects, including also Fallot tetralogy. (12) Among symptomatic variants, without associated diseases, the most common is the constrictive traheo-esofagian vasculo-ligamentar ring.…”

Section: Discussionmentioning

confidence: 99%

Asymptomatic Double Aortic Arch Accidentally Diagnosed for a Child with T-Cell Lymphoma - Case Report

Hălmaciu

Andrei

Sorin

et al. 2018

ARS Medica Tomitana

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Introduction. Double aortic arch (DAA) represents a vascular malformation generated by the persistence of the right dorsal aorta from the intrauterine life. An aortic ring is formed, that surrounds the trachea and esophagus, resulting in difficulty in breathing and swallowing. Case report. We report the case of a 13 years old male child who was admitted to the pediatric surgery department accusing the presence of a paravertebral subcutaneous lesions. Histopathological result of the excised lesion revealed the presence of peripheral T-cell lymphoma. Examination of computer tomography angiography (Angio-CT) revealed the presence of a complete arterial chain (aortic double arch - DAA) around the trachea and esophagus, without signs of compression. Most cases are diagnosed in the first year of life, the literature reports a few cases of DAA diagnosed late, to the adolescent or adult. Clinically most of the anatomical variants are usually symptomatic especially that are associated with congenital heart defects, including also Fallot tetralogy. Conclusions. Angio-CT is a very useful method in diagnosing arterial or venous malformations, symptomatic or asymptomatic.

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A double aortic arch presenting in the 7th decade of life

Cited by 5 publications

References 8 publications

Double Aortic Arch in an Asymptomatic Adult

Double Aortic Arch in an Asymptomatic Adult

Diagnosis and surgical repair of congenital double aortic arch in infants

Asymptomatic Double Aortic Arch Accidentally Diagnosed for a Child with T-Cell Lymphoma - Case Report

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