A "scar" and epilepsy: coup de sabre

Duyff, Ruurd F; Vos, J M I

doi:10.1136/jnnp.65.4.568

Cited by 7 publications

(2 citation statements)

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“…[2][3][4][5][6][7] Ipsilateral abnormalities of brain imaging have been reported in patients with LSCS. 2 4 5 7-9 We report an unusual case of a pregnant woman with preexisting plaque-morphea, newly developed LSCS associated with progressive neurological symptoms, and a rapid response to pulsed corticosteroid treatment.…”

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confidence: 99%

Linear scleroderma "en coup de sabre" coexisting with plaque-morphea: neuroradiological manifestation and response to corticosteroids

Unterberger

Trinka²,

Engelhardt³

et al. 2003

Journal of Neurology, Neurosurgery &Amp; Psychiatry

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A 24 year old woman in the 33rd week of pregnancy developed progressive neurological complications with right sided hemiparesis in association with the occurrence of linear scleroderma "en coup de sabre" (LSCS) and preexisting plaque-morphea, already being treated by balneophototherapy. Further progression of neurological symptoms led to a caesarean section with the delivery of a healthy child. Brain magnetic resonance imaging (MRI) showed focal T2 signal increases in the left frontoparietal region directly adjacent to the area of LSCS. Cerebrospinal fluid analysis revealed oligoclonal bands, suggesting an intracerebral inflammatory process. Subsequent pulsed corticosteroid treatment led to a remission of neurological symptoms and to a marked resolution of the MRI lesions.

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mentioning

confidence: 99%

Linear scleroderma "en coup de sabre" coexisting with plaque-morphea: neuroradiological manifestation and response to corticosteroids

Unterberger

Trinka²,

Engelhardt³

et al. 2003

Journal of Neurology, Neurosurgery &Amp; Psychiatry

View full text Add to dashboard Cite

show abstract

“…Especula-se que as alterações cutâneas são induzidas por malformações cerebrais primárias, sugerindo que a ELGS possa representar síndrome neurocutânea de displasia vascular, similar a síndrome de Sturge-Weber, mais do que uma forma de doença vascular do colágeno localizada (Chung et al, 1995). A hemiatrofia facial já foi reportada em associação com a síndrome de Sturge-Weber (Koch, 1972 (Appenzeller et al, 2004;Asher;Berg, 1982;Aktekin et al, 2005;Carreno et al, 2007;Chang et al, 2004;Chapman et al, 1999;Chung et al, 1995;Cory et al, 1997;David et al, 1991;DeFelipe et al, 2001;Dupont et al, 1997;Duyff;Vos, 1998;Flores-Alavarado et al, 2003;Fry et al, 1992;Gambichler et al, 2001;Goldberger-Stern et al, 1997;Grosso et al, 2003;Higashi et al, 2000;Holl-Wieden et al, 2006;Holland et al, 2006;Kasapcopur et al, 2003;Ledeman, 1984;Liu et al, 1994 (Ahn et al, 1996;Julian;Bowera, 2003).…”

Section: Revisão Da Literatura 46unclassified