Carotid artery dissection is a cerebrovascular disease, the cause of which is assumed to be connective tissue dysplasia. The provoking factors may be injury, infections, high-intensity sports. This disease can occur both asymptomatically and manifest itself with various neurological symptoms (headache, Gorner syndrome). In our clinical case, the young patient showed no signs of connective tissue dysplasia, nor provoking factors. Timely diagnosis contributed to the rapid determination of arterial dissection, and early treatment provided stabilization of the patient’s condition and regression of neurological deficit. The literature data on the diagnosis and treatment of the disease are presented.