Acute sensorineural hearing loss associated with aortitis syndrome

Yasui, Takuya; Yamasoba, Tatsuya

doi:10.1080/03655230701596392

Cited by 7 publications

(5 citation statements)

References 12 publications

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“…Only a few cases in the literature reported an association of TA with SNHL [ 82 – 84 ]. Hearing loss is often progressive, although it can be stable or fluctuating; is usually bilateral and asymmetric; develops over several weeks to months; and mainly involves high frequencies.…”

Section: Inner Ear Involvement In Autoimmune Diseasesmentioning

confidence: 99%

Audiovestibular Symptoms in Systemic Autoimmune Diseases

Ralli

D’Aguanno

Stadio

et al. 2018

Journal of Immunology Research

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Immune-mediated inner ear disease can be primary, when the autoimmune response is against the inner ear, or secondary. The latter is characterized by the involvement of the ear in the presence of systemic autoimmune conditions. Sensorineural hearing loss is the most common audiovestibular symptom associated with systemic autoimmune diseases, although conductive hearing impairment may also be present. Hearing loss may present in a sudden, slowly, rapidly progressive or fluctuating form, and is mostly bilateral and asymmetric. Hearing loss shows a good response to corticosteroid therapy that may lead to near-complete hearing restoration. Vestibular symptoms, tinnitus, and aural fullness can be found in patients with systemic autoimmune diseases; they often mimic primary inner ear disorders such as Menière's disease and mainly affect both ears simultaneously. Awareness of inner ear involvement in systemic autoimmune diseases is essential for the good response shown to appropriate treatment. However, it is often misdiagnosed due to variable clinical presentation, limited knowledge, sparse evidence, and lack of specific diagnostic tests. The aim of this review is to analyse available evidence, often only reported in the form of case reports due to the rarity of some of these conditions, of the different clinical presentations of audiological and vestibular symptoms in systemic autoimmune diseases.

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Section: Inner Ear Involvement In Autoimmune Diseasesmentioning

confidence: 99%

Audiovestibular Symptoms in Systemic Autoimmune Diseases

Ralli

D’Aguanno

Stadio

et al. 2018

Journal of Immunology Research

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“…Kanzaki et al [10] reported six cases of steroiddependent SNHL associated with TAK. Yasui and Yamasoba [9] also reported that corticosteroid therapy was effective in improving the hearing in 14 out of 20 cases of SNHL associated with TAK. In our case, although corticosteroid therapy was ineffective after the onset of severe bilateral hearing loss, antecedent Meniere's disease-like symptoms seemed to be partially controlled with prednisolone and methotrexate.…”

Section: Discussionmentioning

confidence: 99%

“…Another possible cause is the immune-mediated inflammatory process in the membranous labyrinth [5,9]. Kanzaki et al [10] reported six cases of steroiddependent SNHL associated with TAK.…”

Section: Discussionmentioning

confidence: 99%

“…Due to the scarcity of TAK cases, whether the hearing loss that occurs in patients with TAK is really a rare manifestation or in fact a common manifestation that has only rarely been reported is unclear. Recently, Yasui and Yamasoba [9] described two of their own patients and reviewed 27 previously reported cases of SNHL associated with TAK. Of these 29 cases, 25 (86%) were female, and 23 (79%) were in the fourth and fifth decades of life.…”

Section: Discussionmentioning

confidence: 99%

“…Sensorineural hearing loss (SNHL) is a well-recognized manifestation of various systemic vasculitides, such as antineutrophil cytoplasmic antibody (ANCA)-associated vasculitides [3,4] and Cogan's syndrome [2]; however, in patients with TAK, only a few cases of SNHL have been reported in the English literature. Accordingly, the pathogenesis remains poorly understood, and there is no established treatment strategy for SNHL [5][6][7][8][9][10][11]. We herein report the clinical findings in a patient with TAK who developed sudden bilateral deafness and underwent bilateral cochlear implants.…”

Section: Introductionmentioning

confidence: 94%

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Bilateral cochlear ossification in a patient with Takayasu arteritis

Mori

Kawashima

Takahashi

et al. 2017

Acta Oto-Laryngologica Case Reports

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Takayasu arteritis (TAK) is a rare type of noninfectious, systemic vasculitis of unknown etiology. A 45-year-old female diagnosed with TAK complained of acute onset bilateral deafness. Auditory tests revealed complete deafness in both ears. Magnetic resonance imaging with fluidattenuation inversion recovery of her temporal bone demonstrated high signal intensity in the whole cochlea and vestibule in both ears. Computed tomography carried out 10 months after the onset of bilateral deafness revealed prominent ossification localized in the area around the modiolus in both cochleae. The patient underwent cochlear implantation in both ears. The cochlear lumens were narrowed and filled with scar tissue, which hindered the insertion of an electrode in both ears. In TAK, cases associated with bilateral severe to profound SNHL where corticosteroid therapy is ineffective in improving hearing, cochlear implantation should be considered within a reasonable period to avoid the difficulty of electrode insertion associated with cochlear ossification. ARTICLE HISTORY

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