An abnormally large prostatic utricle cyst associated with unilateral renal agenesis

Abstract

Prostatic utricle cyst is an uncommon congenital disorder associated with urogenital anomalies. We present a case of an abnormally large prostatic utricle cyst filling the whole of the abdominal cavity with unilateral renal agenesis in an 8-year-old male child.

Klinefelter syndrome presenting with perinatal ascites associated with unilateral renal agenesis and a prostatic utricle cyst

“…Other possible differential diagnoses include prostatic utricle cyst, Mullerian duct cyst, bladder diverticulum, ectopic ureter, dilated ejaculatory duct, seminal vesicle cysts or urachal cysts 2. Utricle cysts are often diagnosed in the first and second decade of life, while Mullerian duct cysts are often diagnosed in the third to fourth decade 5. Zinner syndrome can also be a differential diagnosis in view of the absence of one kidney in our case, a characteristic finding of this syndrome with seminal vesicle cyst and ejaculatory duct obstruction 10…”

“…The incidence of prostatic utricle cyst is approximately between 11% and 14% in association with distal hypospadias or disorder of sexual differentiation anomalies and up to 50% in the presence of perineal hypospadias 2 3. It is also commonly associated with other congenital abnormalities such as unilateral renal agenesis, cryptorchidism, rectourethral fistula and Down syndrome 4 5. It occurs in up to 4% of neonates and 1% of adults and is often asymptomatic unless it is markedly enlarged, causing obstructive symptoms or infertility 5.…”

“…It is also commonly associated with other congenital abnormalities such as unilateral renal agenesis, cryptorchidism, rectourethral fistula and Down syndrome 4 5. It occurs in up to 4% of neonates and 1% of adults and is often asymptomatic unless it is markedly enlarged, causing obstructive symptoms or infertility 5. Antenatal diagnosis of prostatic utricle is infrequent 6…”

An unusual case of LUTS in an adolescent man: a case report and literature review

“…They are detected earlier in life, around the first and second decade in contrast to Mullerian cysts. There is an association with prostatic utricle cysts and genitourinary abnormalities including unilateral renal agenesis (10-25%) and hypospadias (25%), 5 whereas Mullerian duct cysts have no associations. 4 The contents of cystic lesions can also provide a clue as to their origin.…”