Anatomic classification of the right aortic arch

Prabhu, Sudesh; Mehra, Siddhant; Kasturi, Srikanth; Tiwari, Rishi; Joshi, Abhijit; Chen, John; Karl, Tom R.

doi:10.1017/s1047951120003601

Cited by 8 publications

(7 citation statements)

References 21 publications

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“…Patency of the distal left arch is important for distinguishing a complete DAA from an incomplete DAA, where this segment is atretic, with the persistence of a fibrous cord that is normally not distinguishable in CT imaging. Instead, total involution of this segment configures a situation of right-sided aortic arch with mirror-branching, which is rarely associated with presence of a vascular ring [ 11 , 12 ].…”

Section: Discussionmentioning

confidence: 99%

A rare case of symptomatic vascular ring

Chiocchi¹,

Laudazi²,

Leomanni³

et al. 2023

Radiology Case Reports

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Section: Discussionmentioning

confidence: 99%

A rare case of symptomatic vascular ring

Chiocchi¹,

Laudazi²,

Leomanni³

et al. 2023

Radiology Case Reports

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“…A more recent study has subclassified RAA into 10 distinct variants. 15 The most frequent variant is mirror-image branching (59.3%–84.5%), followed by ALSA (14.1%–39.9%), then isolated left subclavian (1%). 3 , 14 …”

Section: Discussionmentioning

confidence: 99%

“…5 Mirror image RAA is frequently seen with Tetralogy of Fallot in 85%–90% of cases. 3 , 6 , 15 Infants present with symptoms of cyanotic heart defects or respiratory distress and poor feeding/weight gain due to compression of the esophagus or trachea. 5 , 6 Conversely, RAA-ALSA is associated with congenital cardiac anomalies in only 5%–15%, thus many with the ALSA variant will go undetected and are typically diagnosed incidentally on imaging during adulthood.…”

Section: Discussionmentioning

confidence: 99%

Subclavian steal syndrome in a right aortic arch with aberrant left subclavian artery atresia

Nakata¹,

Stahlfeld²,

Simone³

2023

SAGE Open Medical Case Reports

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Congenital aortic arch anomalies are an uncommon diagnosis resulting from embryologic malformations during the fourth to eighth week of gestation. Asymptomatic variants frequently are overlooked in the perinatal period and diagnosed incidentally during adulthood. Symptomatic variants can present with steal syndrome or dysphagia lusoria. The right aortic arch is a rare anomaly that is usually associated with other congenital anomalies but can occur in isolation. The most common types of right aortic arches are mirror image branching or an aberrant left subclavian artery. Aortic arch anomalies are important to recognize as they may have important implications in management. We present a 74-year-old female with a right aortic arch and aberrant left subclavian artery that was discovered after a fall. An extensive evaluation and work-up revealed symptoms consistent with subclavian steal syndrome that resolved following a carotid-axillary bypass. Subclavian steal secondary to a right aortic arch is extremely rare. This report reviews the current literature of a right aortic arch with an aberrant left subclavian artery presenting as a subclavian steal syndrome.

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“…3 In a study by Prabhu et al, 10 variations of the right aortic arch, which arises from the fourth right pharyngeal arch artery, were identified, with potential embryological causes. 10 This classification excludes right arches originating from structures other than the right fourth pharyngeal arch vessel, such as the right-sided cervical aortic arch, as well as right arches containing the circumflex aorta. The classification remains the same whether a right-sided arterial duct is present or not.…”

Section: Discussionmentioning

confidence: 99%