Arrhythmogenic right ventricular dysplasia / THE DARK VOYAGE OF THE FEARLESS EAGLE /Case presentation and review of the literature

Abstract

An 18 years old female died suddenly while sunbathing. Her family consulted an electro physiologist. He scanned the family for long QT, Brugada and ARVD. ECGs were performed on all the family members, which showed PVC's in one of her cousins, for whom a 24 hours recording ECG showed 200 polymorphic PVCs. Echocardiogram was normal, and Signal-Averaged ECG (SAECG) is negative, he adopted a "watch and see" strategy (Figure 1-2).