Caroli Disease: A Case Report Observed at the Cocody Teaching Hospital of Abidjan (Cote D’Ivoire)

Ouattara, A.; Koné, S.; Allah-Kouadio, E.; Soro, D.; Ndjitoyap, A. W.; Kouadio, E.; Kouamé, K.; Fanou, C. D.; Lohouès-Kouacou, M. J.; Camara, B. M.

doi:10.4236/ojgas.2017.71004

Cited by 1 publication

(1 citation statement)

References 11 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Similar findings were observed at Cocody Teaching Hospital of Abidjan by Ouattara et al in Cote D’Ivoire, where a 9-year-old girl presenting with intermittent chronic fever, hepatomegaly, and ascites without abdominal pain or jaundice was diagnosed with Caroli disease [ 13 ].…”

Section: Discussionsupporting

confidence: 82%

A Unique Case of Caroli Disease in Kenya\'s Medical Landscape

Lengoiboni,

Kailani,

Bikoro

et al. 2023

Am J Case Rep

View full text Add to dashboard Cite

Patient: Male, 14-year-old Final Diagnosis: Caroli disease Symptoms: Abdominal pain and fever Clinical Procedure: — Specialty: General and Internal Medicine Objective: Rare disease Background: If a young patient presents with fever, abdominal pain, jaundice and significant imaging abnormalities, especially dilation of the biliary system, it is usually due to obstruction from stones or strictures. However, on very rare occasions, it can be due to complications of congenital cystic dilatation of the biliary system, known as Caroli disease. We present such a patient and discuss the differential diagnosis and implications for long-term management. Case Report: A 14-year-old boy presented to the Emergency Department with a sudden onset of high-grade fever and abdominal pain for 2 weeks, accompanied by vomiting of blood. The patient had no relevant medical history. He was malnourished and had moderate pallor, jaundice, and right upper quadrant pain. Imaging revealed cystic dilatation of intrahepatic ducts and a central dot sign. There were no features suggesting advanced liver disease otherwise, and no tumors or cysts in the kidneys. A diagnosis of Caroli disease was made. The symptoms were ascribed to acute cholangitis and improved with antibiotics. He was discharged home 1 week later. No further blood loss was observed. Conclusions: This case study describes a patient with ascending cholangitis, a complication of Caroli disease. This diagnosis should be considered in the differential diagnosis when a child or young adult presents with features of cholangitis, abnormal biliary imaging, and/or upper gastrointestinal bleeding, or portal hypertension. No prior cases of this disease have been encountered, documented, or published in Kenya. This case can increase awareness among primary care clinicians, including pediatricians.

show abstract

Section: Discussionsupporting

confidence: 82%