Common atrium and the associated malformations

Zhang, Yi; Yang, Zhi‐gang; Yang, Meng‐Xi; Shi, Ke; Li, Rui; Diao, Kai-yue; Guo, Yingkun

doi:10.1097/md.0000000000012983

Cited by 5 publications

(2 citation statements)

References 26 publications

(36 reference statements)

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“…A single atrium is a very rare condition characterized by an embryologically deficient interatrial septum. The morphology of the right atrium (crista terminalis, pectinate muscle, and atrial appendage) is in the dextral part of the common atrium, while the sinistral part has the morphology of the left atrium (smooth non-trabeculated walls and left atrial appendage) [ 3 , 6 , 7 , 8 ]. The prognosis of patients with a single atrium is very poor, having mortality up to 50% even in the highest facility center, as reported by Tabbah et al [ 3 ].…”

Section: Discussionmentioning

confidence: 99%

Situs Inversus Partialis With a Wandering Spleen Having a Single Atrium: A Rare Tale of Survival

Deolikar,

Gemnani,

Saboo

et al. 2023

Cureus

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This case report of a rare condition involving situs inversus partialis, wandering spleen, and a single atrium. Situs inversus partialis is a congenital developmental defect in which the abdominal or thoracic organs are reversed to the opposite side of the body across the sagittal plane. The case report highlights the congenital developmental anomaly and the diagnostic and management complexities associated with this condition. The patient in this case has survived to the age of 24, despite the presence of a single atrium. In the existing literature, situs inversus is a known congenital condition, but partial situs inversus is less common. A wandering spleen is also a rare condition characterized by splenic hypermobility. The combination of situs inversus partialis, a wandering spleen, and a single atrium is particularly unusual and has limited reported cases. Therefore, this research contributes to the existing literature by providing a unique case report and highlighting the challenges associated with diagnosis and management in such cases.

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Section: Discussionmentioning

confidence: 99%

Situs Inversus Partialis With a Wandering Spleen Having a Single Atrium: A Rare Tale of Survival

Deolikar,

Gemnani,

Saboo

et al. 2023

Cureus

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“…Single atrium (SA) is defined as complete or near complete absence of the interatrial septum, and has clinical and hemodynamic similarities with large-size atrial septal defect of fossa ovalis type. [1][2][3] It is a rare form of congenital heart defect accounting for 0.5%-1% of all congenital heart diseases. 4 SA is a term often used interchangeably with common atrium in medical literatures.…”

Section: Introductionmentioning

confidence: 99%

A 78-year-old man diagnosed with single atrium as congenital heart disease

Azaje,

Abebe,

Fentahun

et al. 2023

SAGE Open Medical Case Reports

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Single atrium is a rare congenital heart disease characterized by complete absence of the interatrial septum. It occurs as an isolated cardiac defect, or as a part of skeletal, muscular, ophthalmologic, and vascular malformations to signify congenital syndromes. A 78-year-old male patient presented with generalized body swelling of 2 weeks duration. He had associated shortness of breath, orthopnea, productive cough, and palpitation. Upon physical examination, blood pressure = 150/75 mmHg, pulse rate = 50 bpm, respiratory rate = 24 bpm, and T° = 36.7 °C. He had signs of pleural effusion on left lung field. Cardiovascular examination revealed mean heart rate of 50 beats/min with irregularly irregular pulse rhythm, raised jugular venous pressure, and pansystolic murmur at left lower sternal border. He had tender hepatomegaly, ascites, and pitting leg edema. Chest X-ray showed cardiomegaly, prominent pulmonary trunks, and left-sided pleural effusion. Electrocardiography revealed atrial fibrillation, bifascicular block (right bundle branch block and left anterior fascicular block) with mean heart rate of 50 beats/min. Two-dimensional transthoracic echocardiography showed complete absence of interatrial septum (single atrium) without atrioventricular defect and interventricular communication. Diagnosis of heart failure secondary to congenital heart disease (single atrium) with atrial fibrillation and bifascicular block was made based on clinical and imaging evaluation. Well-tolerated symptoms of a single atrium until late adulthood could be explained by the presence of streaming or incomplete mixing of blood within the atrium, in which the more oxygenated blood is directed to the systemic circuit.

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Low-Dose Dual-Source Computed Tomography for Evaluating Persistent Truncus Arteriosus Associated with Cardiovascular Anomalies: Comparison with Transthoracic Echocardiography

Tang

Wang

Shi

et al. 2021

Preprint

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BackgroundTo assess the morphological features of persistent truncus arteriosus (PTA) on low-dose dual-source computed tomography (DSCT) and compare its diagnostic value for associated cardiovascular anomalies with that of transthoracic echocardiography (TTE).Methods:Twenty-four PTA patients were enrolled in this retrospective study. The types of PTA, diameters of the truncus artery (TA), main pulmonary artery (MPA), right pulmonary artery (RPA), left pulmonary artery (LPA), and ventricular septal defect (VSD) on DSCT were recorded. Besides, all associated cardiovascular abnormalities were assessed. The diagnostic performance of DSCT and TTE for associated anomalies were compared. The effective doses of DSCT were calculated.Results:Four types were found: type A1(n=13/24, 54.17%), type A2(n=7/24, 29.16%), type A3（n=3/24, 12.50%）and type A4(n=1/24,4.17%). The mean diameter of VSD, TA, MPA, RPA, and LPA was 1.47±0.56cm, 3.92±1.56cm, 2.27±1.65cm, 1.48±0.74cm and 1.38±0.66cm, respectively. 78 associated cardiovascular anomalies were confirmed. The most common associated abnormalities were VSD (100%), right-sided aortic arch (33.33%) and aortopulmonary collateral vessels (29.17%). Although TTE was better at diagnosing intracardiac anomalies (accuracy:99.17% vs. 95%; sensitivity: 97.06% vs. 88.24%; specificity: 100% vs. 97.67%), DSCT had an advantage in diagnosing the associated cardiovascular abnormalities (accuracy: 98.61% vs. 96.07%; sensitivity: 94.87% vs. 82.05%; specificity: 99.44% vs. 99.15%). The estimated mean effective doses was 0.98±0.37mSv (＜1mSv). Conclusions:Low-dose DSCT could accurately confirm the morphological features of PTA. Compared to TTE, low-dose DSCT is a better diagnostic tool for associated cardiovascular abnormalities. Combining with TTE will be beneficial to provide more accurate information for clinical interventions.

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Common atrium and the associated malformations

Cited by 5 publications

References 26 publications

Situs Inversus Partialis With a Wandering Spleen Having a Single Atrium: A Rare Tale of Survival

Situs Inversus Partialis With a Wandering Spleen Having a Single Atrium: A Rare Tale of Survival

A 78-year-old man diagnosed with single atrium as congenital heart disease

Low-Dose Dual-Source Computed Tomography for Evaluating Persistent Truncus Arteriosus Associated with Cardiovascular Anomalies: Comparison with Transthoracic Echocardiography

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