Concomitant  en coup de sabre  and plaque type morphea in the same patient: a rare occurrence

Arif, Tasleem; Adil, Mohammad; Amin, Syed Suhail; Sami, Marwa; Raj, Dinesh

doi:10.5114/dr.2017.71222

Cited by 3 publications

(1 citation statement)

References 7 publications

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“…Treatment for the patient was prednisolone 30 mg/day and topical tacrolimus ointment 0.1% to be applied twice daily. After 1 month of treatment, there were no new lesions and the existing lesions over the scalp and thigh showed improvement with respect to thickness and pigmentation [ 34 ].…”

Section: Resultsmentioning

confidence: 99%

Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review

Ulc

Rudnicka

Waśkiel‐Burnat

et al. 2021

JCM

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Scleroderma (morphea) en coup de sabre is a localized subtype restricted to the frontoparietal region of the head. Current treatment paradigms rely on low levels of evidence, primarily case reports and case series-supported by expert opinions. The aim of this article was to systematically analyze current data related to the treatment of localized scleroderma en coup de sabre. The databases Scopus, PubMed, and EBSCO were searched for all reports discussing the treatment of localized scleroderma en coup de sabre. The keywords en coup de sabre, “facial linear scleroderma”, and “morphea linearis”, combined with “treatment” or “therapy” were used as search terms. A total of 34 articles analyzed treatment outcomes for patients with localized scleroderma en coup de sabre including 4 retrospective cohort studies, 2 prospective cohort studies, 4 case series, and 24 case reports, representing a total of 69 patients (38 children and 31 adults). Methotrexate was the most commonly investigated treatment (26 patients) with a highest response rate (26/26, 100%). Other treatments included systemic glucocorticosteroids (nine patients), followed by UVA1 (four patients), mycophenolate mofetil (two patients), hydroxychloroquine (five patients), abatacept (two patients), tocilizumab (three patients), cyclosporine (one patient), interferon gamma (one patient), PUVA therapy (two patients), NB-UVB therapy (one patient), and pulsed dye laser (one patient). Reconstructive and surgery treatment was successfully used for lesions with settled disease activity to improve the cosmetic aspect of the lesions. Conclusion: methotrexate is the most often-studied treatment and reported good clinical outcomes in children and adults with localized scleroderma en coup de sabre.

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Section: Resultsmentioning

confidence: 99%

Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review

Ulc

Rudnicka

Waśkiel‐Burnat

et al. 2021

JCM

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Morphea en coup de sabre and hemifacial atrophy in an interdisciplinary approach

Wróblewska

Polańska

Dańczak‐Pazdrowska

et al. 2020

JoFA

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The increase in the degree of fluctuation asymmetry is accompanied, among others, by diseases such as morphea en coup de sabre (morphea ECDS) or Parry‑Romberg syndrome (PHA). Patients suffering from them struggle not only with dermatological defects, but also with neurological, rheumatological, orthopedic, ophthalmological and dental symptoms. Morphological and functional disorders and craniofacial deformities related to them often generate psychosocial problems. The complexity of the issues to be solved proves the necessity of undertaking interdisciplinary actions aimed at developing objective diagnostic and therapeutic protocols, restoring (especially in pediatric patients) as close as possible to the correct developmental patterns, inhibiting the active phase of the disease and undertaking effective and aesthetically satisfying measures.

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En coup de sabre — a case report of therapeutic difficulties

Szymoniak‐Lipska¹,

Cieplewicz²,

Polańska³

et al. 2020

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En coup de sabre (ECDS) is a rare linear form of localized scleroderma that occurs more frequently in children than in adults. The involvement of the scalp leads to cicatricial alopecia. The aim of this paper is to present a problematic case of ECDS in young female patient. Many terapeutical methods were introduced, based on guidelines described in diagnostic and therapeutic recommendations of the Polish Dermatological Society (e.g. methotrexate, oral and intravenous glucocorticoids, subcutaneous triamcinolone injections and topical high potent steroids as well as kalcineurin inhibitor (tacrolimus). The lasting improvement was not achieved. The remission was finally induced after the implementation of mycophenolate mofetil.

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Concomitant en coup de sabre and plaque type morphea in the same patient: a rare occurrence

Cited by 3 publications

References 7 publications

Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review

Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review

Morphea en coup de sabre and hemifacial atrophy in an interdisciplinary approach

En coup de sabre — a case report of therapeutic difficulties

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