Congenital bilateral ectropion in lamellar ichthyosis

Generalized morphea in a child with harlequin ichthyosis: a rare association

“…5,6 According to the new classification criteria, localized scleroderma has four different subtypes: plaque morphea, GM, linear scleroderma and deep morphea. [8][9][10] The GM is defined by the presence of four or more plaques, with individual plaques greater than 3 cm and involving at least two out of seven anatomic sites, 2 as evidenced in our patient that presented lesions occurring in upper and lower limbs, and trunk.…”

“…The nailfold capillaroscopy was performed without being able to visualize capillaries due to crusts periungual. Therefore, the patient fulfilled the juvenile localized scleroderma criteria (GM subtype) 8 and methotrexate (0.5 mg/kg/week) and prednisone (1.0 mg/kg/day) were introduced at the age of 3 years 11 months. At 4 years and 1 month, methotrexate dosage was increased to 1.0 mg/kg/week.…”

Collodion baby: a case report

“…7,8 Neonates with ectropion are at very high risk of developing keratitis but expert and timely ophthalmic management can prevent the complications. 9,10 The management of the case relies on the timely identification and early institution of intensive care therapy. Intensive care therapy consists of maintaining adequate oxygen saturation, intensive skin care, maintaining body temperature and adequate feeding.…”

Collodion baby-congenital ichthyosis: clinical review

“…Persistent ectropion should be managed surgically or medically with periocular retinoids like tazarotene. 15 The use of systemic retinoids accelerates the shedding of hyperkeratotic plates and improves scaling. Together with enhanced moisturization, electrolyte monitoring in the early neonatal period, sepsis prevention and physiotherapy, long-term survival of 81% has been reported.…”