Congenital H-type tracheoesophageal fistula: A multicenter review of outcomes in a rare disease

Fallon, Sara C.; Langer, Jacob C.; Peter, Shawn D. St.; Tsao, Kuo Jen; Kellagher, Caroline M.; Lal, Dave R.; Whitehouse, Jill S.; Diesen, Diana L.; Rollins, Michael D.; Pontarelli, Elizabeth M.; Malek, Marcus M.; Iqbal, Corey W.; Upperman, Jeffrey S.; Leys, Charles M.; Wulkan, Mark L.; Hill, Sarah J.; Blakely, Martin L.; Kane, Timothy D.; Wesson, David E.

doi:10.1016/j.jpedsurg.2017.05.002

Cited by 48 publications

(53 citation statements)

References 17 publications

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“…Isolated tracheoesophageal fistulas without esophageal atresia, also known has H- or N-type fistulas, have a narrow connection between the trachea and esophagus that is sometimes only seen while the patient is in the prone position. Endoscopy is not 100% sensitive, which may also lead to delayed diagnosis [ 6 ]. Type II-IV laryngeal clefts, on the other hand, have a larger defect that is easily seen on lateral imaging [ 5 ].…”

Section: Discussionmentioning

confidence: 99%

A rare case of laryngeal cleft in association with VACTERL and malrotation

Chen

Stern

Jeremy

et al. 2019

Radiology Case Reports

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We report a rare case of a neonatal girl who presented with coughing and dyspnea immediately after feeds. At birth, she was noted to have an imperforate anus with a posterior fourchette fistula from which she was stooling. Initial imaging with radiography showed a normal bowel gas pattern; however, lumbar vertebral anomalies were noted. An upper GI series was performed and revealed a laryngeal cleft and malrotation. Ultrasound confirmed malrotation with an abnormal SMA-SMV relationship. Since laryngeal cleft is a rare condition and may not be known to most radiologists, its incidence is likely underestimated. It is important to note the association of laryngeal clefts with VACTERL and malrotation. In addition, it is essential not to confuse a laryngeal cleft with a tracheoesophageal fistula since the management differs.

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Section: Discussionmentioning

confidence: 99%

A rare case of laryngeal cleft in association with VACTERL and malrotation

Chen

Stern

Jeremy

et al. 2019

Radiology Case Reports

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“…Die Inzidenz von Nahtinsuffizienzen wird mit 8-18 % angegeben [19,47]. Allgemeingültige, nicht evidenzbasierte Handlungsempfehlungen orientieren sich an der Größe des Defektes und dem Zustand des Kindes.…”

Section: Anastomoseninsuffizienzunclassified

Behandlung der Ösophagusatresie mit unterer tracheoösophagealer Fistel – Zusammenfassung der aktuellen S2K-Leitlinie der DGKCH

Mayer

Gitter

Göbel³

et al. 2020

Klin Padiatr

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ZusammenfassungDie Ösophagusatresie (ÖA) ist eine angeborene Kontinuitätsunterbrechung der Speiseröhre mit oder ohne Fistel zur Trachea (Tracheoösophageale Fistel, TÖF). Je nach Abstand zwischen den beiden Ösophagusenden unterscheidet man eine „kurzstreckige“ von einer „langstreckigen“ Form. Bis zu 50% der Neugeborenen weisen weitere Anomalien auf. Eine pränatale Diagnose der ÖA gelingt in 32–63% der Fälle. Die interdisziplinäre Betreuung dieser Kinder hat sich in den letzten Jahren gewandelt. In der folgenden Arbeit wird die aktuelle S2K-Leitlinie der Deutschen Gesellschaft für Kinderchirurgie zur Behandlung der ÖA mit unterer TÖF, die etwa 90% aller Fälle ausmacht, zusammengefasst. Hierzu gehören das präoperative Management sowie operative und anästhesiologische Aspekte (u. a. Thorakoskopie vs. Thorakotomie, präoperative Tracheobronchoskopie, intraoperative Hyperkapnie und Azidose). Ferner wird das postoperative Management insbesondere von relevanten Komplikationen wie der Anastomosenstenose beschrieben. Trotz Fortschritten in der Behandlung der ÖA ist die Langzeitmorbidität mit Motilitätsstörungen des Ösophagus, gastroösophagealer Refluxkrankheit, rezidivierenden Infektionen der oberen und unteren Atemwege, Tracheomalazie, mangelhaftem Gedeihen sowie orthopädischen Problemen nach Thorakotomie weiterhin hoch. Zum Erreichen einer guten Lebensqualität ist daher eine gute interdisziplinäre Nachsorge wichtig.

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“…Several small case series have shown the thoracoscopic approach to be successful in this rare lesion. 12,13 The recent advent of a 5-mm surgical stapling device has made approaching this lesion thoracoscopically more favorable as well. Three such patients have recently been approached this way with excellent results by two surgeons in the MWPSC.…”

Section: Role Of Thoracoscopymentioning

confidence: 99%

The Current Thoracoscopic Management of Esophageal Atresia

Fraser

Peter

2020

Eur J Pediatr Surg

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The thoracoscopic repair of esophageal atresia with tracheoesophageal fistula is a complex neonatal minimally invasive procedure. The thoracoscopic approach is now nearing its third decade of experience and but is overall still not widely utilized, only in skilled centers and by experienced surgeons. This article will summarize the recent advancements in technique and knowledge in the thoracoscopic approach to this challenging neonatal congenital abnormality.

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Congenital H-type tracheoesophageal fistula: A multicenter review of outcomes in a rare disease

Cited by 48 publications

References 17 publications

A rare case of laryngeal cleft in association with VACTERL and malrotation

A rare case of laryngeal cleft in association with VACTERL and malrotation

Behandlung der Ösophagusatresie mit unterer tracheoösophagealer Fistel – Zusammenfassung der aktuellen S2K-Leitlinie der DGKCH

The Current Thoracoscopic Management of Esophageal Atresia

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