Congenital macular macrovessels

Abstract

In the presence of an aberrant vessel crossing the macular region, visual acuity and ophthalmoscopic and fluoroangiographic findings tend to have remained stable at long-term follow-up.

Congenital Retinal Macrovessel: a Case Report

“…The presence of hemoglobin circulating in the vessel could explain this phenomenon. Shah et al [7] reported reduced retinal sensitivity at the macular area using liquid crystal display microperimetry in a case of congenital retinal macrovessel with no sign of macular edema on OCT. FA findings of anomalous vessels consist of early filling and delayed emptying, capillary perfusion abnormalities, focal capillary dilatations, direct arteriovenous communications and enlargement of the foveal avascular zone [1,3,5,8]. In our case, the retinal macrovessel that originated in the inferotemporal central retinal vein branch crossed the macula and touched the fovea.…”

“…Most congenital retinal macrovessel cases are unilateral and stable with excellent visual prognosis and are detected on routine examination. In rare cases, foveolar cysts, macular hemorrhages, pigmentary changes, serous macular detachment and a displaced fovea may also be seen [1,2,[4][5][6]. These findings can deteriorate VA.…”

“…The FAZ asymmetry was noticed between both eyes. We performed an OCT examination that showed a normal foveal contour, the diameter of the macrovessel and subtle parafoveal thickening without intraretinal fluid accumulation De Crecchio Get al [5]. Reported a case of a macrovessel with decreased vision due to serous retinal detachment of the macula, macular thickening with a preserved foveal contour and distorted retinal microarchitecture on OCT. We also performed a central 30-2 visual field test to support the observed macular changes, but the findings did not correlate with the OCT findings.…”

“…Such vessel supplies or drains the retina both inferiorly and superiorly to the horizontal raphe. Its origin often derives from the vein without a significant clinical symptom and decreased visual acuity [3,5]. In rare cases, a congenital retinal macrovessel can be an artery or an artery and vein together [1][2][3].…”

Letter by Lee et al Regarding Article, “Spontaneous Resolution of Central Serous Chorioretinopathy in a Patient With Congenital Retinal Macrovessel”

“…There are a few more similar cases of CRM combined with macular edema that have been reported previously. 3,4 Nevertheless, this case report is valuable because this is the first well-documented report of what may be a spontaneously resolved CSCR with CRM, and this could provide information about a possible etiologic relationship between CSCR and CRM. Currently, spectral domain OCT techniques have been developed to produce more detailed cross-sectional retinal images and RPE changes in CSCR.…”