Congenitally corrected transposition with mirror-image atrial arrangement

Attié, Fause; Cerda, Juan; Richheimer, Roberto; Chávez-Domínguez, Rafael; Buendı́a, Alfonso; Ovseyevitz, J; Muñóz-Castellanos, Luis

doi:10.1016/0167-5273(87)90006-4

Cited by 9 publications

(2 citation statements)

References 18 publications

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“…Left ventricular outflow tract obstruction can be relieved with a transannular patch in patients with atrial situs inversus with congenitally corrected transposition of the great arteries since they usually have a normally positioned atrioventricular node [7] and the bundle of His runs on the posterior inferior margin of the ventricular septal defect. This contrasts with the congenitally corrected transposition of the great arteries with atrial situs solitus in which the atrioventricular node is located anteriorly adjacent to the right atrioventricular valve orifice with the bundle of His coursing on the anterior right ventricular free wall caudal to the pulmonary annulus.…”

Section: Discussionmentioning

confidence: 99%

Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation

Goyal¹

2012

Turk Gogus Kalp Dama

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Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation Atriyal ve visseral situs inversusla birlikte doğuştan düzeltilmiş büyük damar transpozisyonu olan bir hastada dekstrokardi, ventriküler septal defekt ve pulmoner stenoz birlikteliği: Nadir bir olgu

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Section: Discussionmentioning

confidence: 99%

Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation

Goyal¹

2012

Turk Gogus Kalp Dama

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“…1216 The frequency of atrioventricular block is greater in corrected transposition with usual atrial arrangment than in the mirror-imaged hearts. 8 The differences noted when comparing risks for such disturbances of conduction between the two groups is well explained by the known differences in the disposition of the atrioventricular conduction system. 8 ' 14 " 16 Histological findings suggest that it is the normally positioned atrioventricular node which gives rise to the penetrating atrioventricular bundle in mirror-imaged variants, even in the presence of atrioventricular block.…”

Section: Discussionmentioning

confidence: 99%

Congenitally corrected transposition with atrioventricular septal defect

Attié

Iturralde²,

Zabal³

et al. 1998

Cardiol Young

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We describe 4 cases of congenitally corrected transposition associated with atrioventricular septal defect, diagnosed by echocardiography and angiocardiography. Two had usual atrial arrangement and two had mirror imaged atrial arrangement . All cases were associated with subpulmonary valvar stenosis. All patients presented with cyanosis and were in sinus rhythm. Atrioventricular septal defect with common atrioventricular junction was easily diagnosed on the basis of a common atrioventricular valve permitting interatrial and interventricular communications. All patients had balanced right and left ventricles. The echocardiographic recognition of the ventricles was based on the presence of the moderator band within the morphologically right ventricle, the characteristics of the apical septal trabeculations, and the shape of the ventricles. Angiocardiographic recognition of the ventricles was achieved on the basis of right and left ventriculography. In one case with usual atrial arrangement, we recorded two His bundle potentials, one anteriorly and another posteriorly. Atrial stimulation revealed blocked atrioventricular conduction at the level of the posterior bundle, and normal atrioventricular conduction through the anterior bundle. In both cases with atrial mirror-imagery, only a posterior His bundle potential was found, with normal atrioventricular conduction revealed by atrial stimulation The clinical course with this combination depends on the other lesions present in addition to the common atrioventricular valve. Our electrophysiological studies show that the conduction system in presence of a common atrioventricular valve is as expected for congenitally corrected transposition with two atrioventricular valves.

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Congenitally Corrected Transposition of the Great Arteries

Hoffman

2009

The Natural and Unnatural History of Congenital Heart Disease

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DescriptionA 60-year-old woman initially presented 8 years ago with atypical chest pain and palpitations.Her 12-lead ECG demonstrated complete heart block, following which she underwent dualchamber pacemaker implantation. She also had transthoracic echocardiogram, which was felt to be technically difficult due to body habitus. She was diagnosed to have mild mitral valve regurgitation, due to mild mitral valve prolapse, and was kept under annual surveillance. There was no other significant medical history. Her last TTE was done a year ago and she had been symptom-free up to her recent clinic visit. Her repeat TTE showed apically displaced Ebstein-like left atrioventricular valve (AV) with tricuspid valve morphology (confirmed by three-dimensional (3D) echo) and heavily trabeculated morphologically right ventricle on the left side of the heart (figures 1, 2, 3 and 4, online supplementary video 1 and supplementary video 2). Her systemic ventricle was mild to moderately impaired, and the tricuspid, left AV was moderately regurgitant. There are no obvious shunt and no other significant valvular abnormalities identified on this recent study. The above findings (atrioventricular and ventriculoarterial discordance) were in keeping with congenitally corrected transposition of great arteries (CC-TGA).CC-TGA is a rare congenital heart defect accounting for <1% of all congenital heart diseases. 1They are usually associated with ventricular septal defect, pulmonary stenosis, Ebstein-like malformation of the systemic AV valve and high-degree AV block. Patients without coexistent shunts are usually asymptomatic and usually diagnosed from investigations like ECG, chest X-ray and TTE done for other reasons. This condition is often missed because of the failure to recognise the above anatomical variation, as in our case.2 Patients with CC-TGA require regular long-term follow-up as Congenitally corrected transposition of great arteries

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Congenitally corrected transposition with mirror-image atrial arrangement

Cited by 9 publications

References 18 publications

Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation

Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation

Congenitally corrected transposition with atrioventricular septal defect

Congenitally Corrected Transposition of the Great Arteries

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