Cor triatriatum in a young woman with syncope

Abstract

DESCRIPTIONA 28-year-old woman presented with recurrent syncope, usually precipitated by anxiety.On examination, she had a low blood pressure of 112/72 mm Hg with normal heart sounds and showed no features suggestive of genetic abnormalities. ECG, Holter and treadmill stress tests were normal. Transthoracic ( fi gure 1 ) and transoesophageal ( fi gure 2 ) echocardiography demonstrated non-obstructive cor triatriatum. A diagnosis of vasovagal syncope with incidental cor triatriatum was made.Cor triatriatum consists of a fi bromuscular membrane dividing the left atrium into a posterosuperior chamber receiving blood from the pulmonary veins and an anteroinferior chamber containing the left-atrial appendage and mitral orifi ce. It represents 0.4% of congenital cardiac anomalies, 1 and is associated with other cardiac defects in 70-80% of cases, 2 anomalous pulmonary venous drainage being the most common. Echocardiography is crucial to determine the transmembrane gradient, pulmonary vein drainage and associated defects.

Cor triatriatum: a single institution's experience

“…[11,12] Tedavi edilmeyen hastalarda mortalite oranı %75'dir. [13] Cerrahi sonrası ölüm oldukça nadirdir. Cerrahi sırasında veya sonrasında ölüm gerçekleşmişse bu durum genellikle eşlik eden diğer kardiyak defektlere bağlıdır.…”