Dyschondrosteose

Felman, Alvin H.

doi:10.1001/archpedi.1970.02100090103009

Cited by 20 publications

(1 citation statement)

References 6 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…In many cases there is a hereditary component with autosomal dominant inheritance of variable penetrance. [1][2][3][4] Several authors have reported the Madelung deformity as being one of the predominant features of dyschondrosteosis, [5][6][7][8][9][10] but this does not account for all cases and other bone dysplasias have also been associated with the condition. 1,11 The aetiology of the premature fusion of the growth plate is unclear and various causes have been suggested including the occupation or nutrition of the patient, [12][13][14][15][16] vascular insufficiency affecting the interosseous pedicle of the distal radial growth plate, 17 muscular disorders 1,18,19 and fibrous bands tethering the distal radial epiphysis.…”

mentioning

confidence: 99%

Osteotomy of the radius and ulna for the Madelung deformity

Reis

Katchburian

Faloppa

et al. 1998

The Journal of Bone and Joint Surgery

View full text Add to dashboard Cite

Correspondence should be sent to Mr M. V. Katchburian at 129 Old Dover Road, T he Madelung deformity can result in pain and decreased function of the wrist and hand. None of the surgical techniques available has been shown consistently to improve grip strength, range of movement or relieve pain. In this prospective study we have treated 18 patients with the Madelung deformity (25 wrists) by wedge subtraction osteotomy of the radius and shortening of the ulna. Our results show statistically significant improvement in grip strength and range of movement of the wrist and forearm. Pain improved in 80% of the patients and 88% were satisfied with the appearance. One patient had a wound infection and another developed reflex sympathetic dystrophy. Two had some recurrence due to continued growth of the ulna and it is recommended that the procedure be delayed until skeletal maturity, or else combined with epiphysiodesis of the ulna.

show abstract