Ebstein’s Anomaly in the Elderly

Cabin, Henry S.; Wood, Thomas; Smith, J. Orson; Roberts, William C.

doi:10.1378/chest.80.2.212

Cited by 13 publications

(2 citation statements)

References 12 publications

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“…The anomaly may lead to the death of the patient early in life (Cabin et al, 1981), but in rare instances survival up the eighth decade has been reported (Cabin et al, 1981;Adams et al, 1956). In case number three there was a subvalvular muscular aortic stenosis which caused a 15 mmHg gradient at rest.…”

Section: Anatomical Variationsmentioning

confidence: 98%

Surgical Intervention in Cases of Ebstein's Anomaly:Abnormal Origin and Structure of the Tricuspid Valve

Mattila

Harjula

Kyllönen

et al. 1982

Scandinavian Journal of Thoracic and Cardiovascular Surgery

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During the ten-year period 1972-81 four patients, two men and two women, with Ebstein's disease underwent operation at our institution. Their average age was 34. Central cyanosis at rest, clubbing and polycythaemia were the most common clinical features of the patients. Enlarged heart, a small pulmonary arterial arch and transluminal lung fields were seen in chest X-ray. Operative findings were a grossly enlarged right atrium and ventricle, the latter having a segment that was typically atrialized and thin-walled but was contracting synchronously with the true right ventricle, and a wide variation in the leaflets of the tricuspid valve and their origins. The atrial septal defect was small in all cases. Artificial heart valves (1 Cutter-Smeloff, 2 Björk-Shiley, 1 St. Jude) were used in the tricuspid reconstruction in addition to closure of the ASDs. One of the patients died postoperatively, the other three are doing well.

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Section: Anatomical Variationsmentioning

confidence: 98%

Surgical Intervention in Cases of Ebstein's Anomaly:Abnormal Origin and Structure of the Tricuspid Valve

Mattila

Harjula

Kyllönen

et al. 1982

Scandinavian Journal of Thoracic and Cardiovascular Surgery

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“…There is an astonishing longevity noticed in patients with Ebstein's anomaly with a survival into eighth and nineth decades [86]. The oldest recorded patients with Ebstein's anomaly lived to 85 years, without cardiac symptoms until the age of 79 years [87].…”

Section: Outcomementioning

confidence: 99%

Ebstein's Anomaly—An Overview

Muthiah¹

2018

CRCM

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Aim: To present the various echocardiographic spectrum of Ebstein's malformation in adolescence and adults. Introduction: Ebstein's anomaly has different anatomic and hemodynamic variables with clinical manifestations of cyanosis, right-sided heart failure and arrhythmias. The leaflet tethering and dysplasia, together with dilatation of the tricuspid valve ring, constitute the anatomic cause of tricuspid regurgitation observed in this condition. Case Reports: The spectrum of leaflet tethering from mild to extreme with varying degrees of tricuspid regurgitation were documented by echocardiography in a 16-year-old cyanotic male with Ebstein's anomaly associated with an atrial septal defect and mild low tricuspid regurgitation (TR), 22-year-old acyanotic male with right-sided heart failure due to severe tricuspid regurgitation and an intact atrial septum, 55-year-old asymptomatic female with moderate high tricuspid regurgitation. The extreme form was described as an "atretic" membrane in a 28-year-old cyanotic male and as a "blanket" of leaflet tissue in a 30-year-old cyanotic male. Conclusion: Ebstein's anomaly has to be suspected clinically in presence of cyanosis with a WPW (Wolf-Parkinson-White) or atrioventricular (AV) block pattern of ECG and its management is complex and must be individualized. RV (right ventricular) exclusion procedures are preferred in advanced cases.

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