Epidermolysis Bullosa

Abstract

There are skin rashes, lesions, and disorders in the neonatal period that require emergent assessment and consultation. A neonate presented with epidermolysis bullosa and provided an opportunity for learning about this condition and various dermatologic resources, primarily DermAtlas. The neonate with suspected epidermolysis bullosa that is delivered in a community setting usually requires transport to a neonatal intensive care unit with pediatric subspecialty care. A case study involving the transport of a neonate with this condition is reviewed, followed by a discussion of the etiology, incidence, pathogenesis, diagnosis, and nursing care before and during transport and parental considerations. The resources available in the neonatal community, primarily DermAtlas, for the identification of epidermolysis bullosa and other dermatological conditions is explored.

Pediatric epidermolysis bullosa - psychosocial impact and the importance of palliative care based on 5 clinical cases

“…This reminds us that the choice to use corticosteroids should be judicious, because even in the topical formulation it can have permanent secondary effects. In fact, treatment should be based essentially on disinfection and wound care 12 .…”

“…Quality of life (QoL) scores have been reported to be lower in these patients, including studies in children and their caregivers 9 , given the challenges that this disease raises. Since there is no curative therapy for EB, an holistic palliative care approach, with wound care and pain management, as well as psychosocial support, is of crucial importance for these patients [10][11][12] .…”