Epidermolysis bullosa acquisita: A heterogeneous disease

Disseminated Cicatricial Pemphigoid

“…Localized chronic head, neck, + ± pemphigoid [3] mucosa of mouth Disseminated generalized + ± cicatricial pemphigoid [14] show similar clinical and electron micros copical findings [7,11,12,15,16]. The rela tions between these two clinical entities however remain controversial and need fur ther investigation [5,12], As far as seen from the relatively few cases, the following criteria to differentiate can be established (table II).…”

“…The rela tions between these two clinical entities however remain controversial and need fur ther investigation [5,12], As far as seen from the relatively few cases, the following criteria to differentiate can be established (table II).…”

Use of intravenous immunoglobulin therapy in autoimmune blistering diseases

“…11.018 skin and multiple mucous membranes. These diseases have several features in common [1][2][3][4][5][6]. They often involve the skin and one or more mucous membranes, which are derived from the stratified squamous epithelial.…”

Differential Diagnosis of Autoimmune Bullous Diseases in the Elderly

“…Inflammatory epidermolysis bullosa acquisita may be indistinguishable from bullous pemphigoid [32]. The non-inflammatory mechanobullous form of epidermolysis bullosa acquisita [33][34][35][36][37][38][39] may be indistinguishable from porphyria cutanea tarda and pseudoporphyria. Mucous membrane pemphigoid [40] is clinically indistinguishable from anti-epiligrin disease, mucosal epidermolysis bullosa acquisita, mucosal linear IgA disease and occasionally mucosal lichen planus.…”

“…Mucous membrane pemphigoid [40] is clinically indistinguishable from anti-epiligrin disease, mucosal epidermolysis bullosa acquisita, mucosal linear IgA disease and occasionally mucosal lichen planus. Bullous systemic lupus erythematosus [41][42][43] may be indistinguishable from epidermolysis bullosa acquisita [33][34][35][36][37][38][39], linear IgA disease [44,45] and bullous pemphigoid.…”