Familial congenital bundle branch system disease

Husson, George S.; Blackman, Marie S.; Rogers, Mark C.; Bharati, Saroja; Lev, Maurice

doi:10.1016/s0002-9149(73)80148-1

Cited by 40 publications

(3 citation statements)

References 13 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…13 It has been suggested that the abnormalities in conduction may reflect inherited congenital abnormalities of parts of the conduction system during development, or hereditary tendencies towards congenital or neonatal degeneration of parts of the conduction system. These developmental abnormalities or tendencies may lie in the conduction system, in the tissues around it and secondarily involving it, or in the vascular or neural supply, 14 and may only become manifest with ageing. 12 In a small proportion of cases the fibrosis of the bundle branch might be due to a simple exaggeration of the ageing changes.…”

Section: Discussionmentioning

confidence: 99%

Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Sarubbi

Gerlis

et al. 1999

Cardiol Young

View full text Add to dashboard Cite

An apparently healthy man of 26 years of age suddenly died. He was known to have had a small ventricular septal defect and complete right bundle branch block from early childhood. At post-mortem examination the small ventricular septal defect was found associated with an aneurysm of the membranous septum. Histological examination showed a normal atrioventricular node and bundle, adjacent to the aneurysm. There was fibrous interruption at the commencement of the right bundle branch, which was considered the basis of the bundle branch block. It was also considered that the right bundle branch block was of the hereditary type and that this, rather than the aneurysm of the membranous septum, was responsible for the unexpected death.

show abstract

Section: Discussionmentioning

confidence: 99%

Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Sarubbi

Gerlis

et al. 1999

Cardiol Young

View full text Add to dashboard Cite

show abstract

“…In children, left anterior hemiblock maybe associated with ischemic myocardial injury as in anomalous origin of the left coronary artery from the pulmonary artery or it may follow cardiac surgery, particularly closure of ventricular septal defect or left ventricular overflow tract myectomy . It may rarely occur as an isolated finding in patients with a family history of conduction disease [6,11] or be associated with lentiginosis [13] .…”

Section: Discussionmentioning

confidence: 99%

Left-axis deviation in otherwise healthy children

Sharratt

Virmani

1985

Pediatr Cardiol

View full text Add to dashboard Cite

Eighteen children with left-axis deviation on the electrocardiogram but no other detected abnormalities are reported. The implications of this finding are discussed. No untoward cardiovascular events occurred during the period of follow-up and the electrocardiographic findings remained unchanged. This, therefore, appears to be a benign entity in the short term but longer follow-up is required before the ultimate prognosis can be determined.

show abstract

“…block seen at birth, carries a poor prognosis: neonatal death is not unusual (Sarachek & The proband was submitted for examination Leonard 1972, Husson et al 1973). because of clinical signs of cardiac disease, This paper describes a family in which and because of a family history of cardiocardiac arrhythmias and pump failure fre-myopathy.…”

Section: Methodsmentioning

confidence: 99%

Familial cardiomyopathy: Autosomally, dominantiy inherited congestive cardiomyopathy with two cases of septal hypertrophy in one family

et al. 1979

View full text Add to dashboard Cite

A family with inherited congestive cardiomyoipathy is presented. The diagnosis is based on clinical, morphological and laboratory evaluations. The first observed sign of the disease is arrhythmia and/or conduction defects. The onset of symptoms of pump failure is in adult life, and affected persons die within several years. Three persons have died suddenly. Septal hypertrophy was present in two affected persons. The mode of transmission is probably autosomal dominant. The recognition of arrhythmia as an early sign of the disease offers the opportunity of an early diagnosis.

show abstract

Familial congenital bundle branch system disease

Cited by 40 publications

References 13 publications

Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Left-axis deviation in otherwise healthy children

Familial cardiomyopathy: Autosomally, dominantiy inherited congestive cardiomyopathy with two cases of septal hypertrophy in one family

Contact Info

Product

Resources

About